DR. DEEPTHI RH

DR.DR SIRISHA VINZAMURI

Abstract

Ichthyosis is an inherited skin disorder (also called disorders of keratinization) that is characterized by hyperproliferation of cells and thus an abnormal physical barrier and manifests as dry, scaly, and thickened skin. Lamellar ichthyosis (LI) is one of the subtypes and has an autosomal recessive inheritance. It is a rare condition where babies present with the shedding of skin and is usually generalized. They are also called “collodion babies” as they are said to have shiny armor of shed skin. Here we present a case of a newborn baby diagnosed with LI and bilateral ectropion which spontaneously reduced after topical treatment such as lubricants and antibiotics were started. We are reporting this case as LI is considered to be a rare inherited disorder and the bilateral ectropion was found to reduce spontaneously without any invasive interventions.