DR. S. SIVARANJANI

DR. MANAVI DEOKRISHNA SINDAL

Abstract

we report a case of a 3 months old female who presented for retina examination with multiple black coloured lesions involving through out the body except face and scalp. The patient was diagnosed as Incontinentia pigmenti with grade 3 skin lesions. The patient was on sodium fusidate ointment over skin twice a day since her 3 days of birth. Her neurological examination was normal. In both eyes anterior segment examination was normal with brisk pupillary reaction. Fundus examination in right eye revealed avascular retina temporally with tufts of neovascularization found at the edges of the avascular retina. Left eye retina was normal. Retinal laser photocoagulation was done in right eye to the avascular retina from neovascular tufts to ora. Complete regression of new vessels was noted on one month follow up. Incontinentia pigmenti is an uncommon disorder affecting females. Early screening and laser treatment have shown to possibly prevent blindness due to retinal detachment.