Dr. RAMYA APPANRAJ

DR. SHISHIR VERGHESE, DR. MAHESHWARI S, DR. GEORGE J. MANAYATH

Abstract

A 63-year-old female presented with complaints of diminution of vision in the left eye (LE) for the past 6 months. Her best corrected visual acuity (BCVA) was 20/20 in the right eye (RE) and 20/125 in LE. Based on fundus examination and multimodal imaging findings, both eyes (BE) were diagnosed to have sector retinitis pigmentosa and an associated active extramacular polypoidal choroidal vasculopathy (PCV) in LE. Spectral domain optical coherence tomography (SD-OCT) also revealed choroidal thinning in BE. Patient underwent bevacizumab injection in the LE. At 1 month follow up, her BCVA remained stable in the LE and SD-OCT showed reduction of sub retinal fluid and size of the polyp. This is the first case report which highlights the association of PCV a pachy choroid disease with RP, in the setting of thin choroids and the importance of multimodal imaging to measure choroidal vascularity index and also to differentiate from CNV and it also postulated a hypothesis for the same.