DR. SOHAM PAL

DR. MD. SHAHID ALAM

Abstract

Aim: To report two rare cases of congenital orbital fibrosis-a distinct clinical entity first described by Mavrikakis et al in 2009.Methods: Retrospective case series of 2 patients with congenital orbital fibrosis.Both patients were evaluated and treated at a tertiary eye care hospital.Results: Blepharoptosis, eyelid retraction, enophthalmos, presence of adiffusely infiltrating orbital mass with secondary involvement of extraocular muscles were presenting features. One patient underwent exploration of the orbit, release and biopsy of scar tissue.Other was treated conservatively for the amblyopia.Conclusion: Congenital orbital fibrosis is a nonfamilial, nonprogressive, unilateral, distinct clinical entity, characterized by the presence of a diffusely infiltrating orbital mass with secondary involvement of extraocular muscles resulting in variable symptomatology due to the cicatricial process.Management of such cases becomes difficult owing to varying features in each case.