DR. RATNAPRIYA SRIVASTAVA

Abstract

PURPOSE

To report a case of a phthisis bulbi with severe mechanical ptosis due to congenital Plexiform Neurofibromatosis.

METHOD

Informant Mother.

A 4-year-old female baby presented with unable to open left eyelid since birth and swelling of left forehead since birth. A detailed ocular examination and relevant laboratory investigations were done. Oculopalsty surgeries were planned with nil visual acuity and explained:

Stage 1- Left eye enucleation with implant

Stage 2- Left eye debulking with upper lid reconstruction

Stage 3- Left tarsofrontal sling surgery.

According to plan, surgeries were performed.

RESULT

After the surgeries, disfigurement of left eye is reduced.

CONCLUSION

In this patient, though the visual outcome was nil surgeries were performed with the interest of cosmetic purpose.