DR. SHILPA DAS

DR. SADANANDA S. SHETTY, DR. ROHIT SHETTY

Abstract

A 33-year old man presented with sudden loss of vision and pain in right eye. He had short stature, small cranium and poor coordination, clinically s/o microcephaly. Right eye showed severe corneal edema with anterior protrusion and underlying break in descemet’s membrane s/o acute hydrops. Vision was not accurately quantifiable due to poor intellect. A C3F8 descemetopexy with compression sutures was done under GA; topical hyperosmotics, anti-glaucoma and steroids were given. Suture removal was done at 5 months. At 7 months, ASOCT showed complete resolution of corneal edema in right eye with scarring; topography showed steep cornea but no evidence of frank keratoconus in left eye. Patient was free from pain and had ambulatory vision. Visual rehabilitation in right eye in the form of contact lens or keratoplasty may be planned with extreme caution in view of high likelihood of amblyopia, requirement of repeated GA procedures, inadequate maintenance of corneal graft and/or contact lens.