DR. SATYABRATA JENA

DR. GAYATRI DEVI PALO

Abstract

Sickle cell retinopathy is an ocular manifestation of sickle cell disease,an inherited group of hemoglobinopathy with systemic and ocular presentations.It is commonly associated with sickle cell disease with homozygous mutation involving both the genes and rarely with sickle cell trait with one defective gene.

Here we present a case of 33 year female with sickle cell trait presented with gradual and painless diminution of vision.On examination,visual acuity in left eye is 6/24 and 3/60 in the right eye.On slit lamp examination,there was comma shaped blood vessel in both the eyes. On fundoscopy,there is tortuosity of vessels,splinter hemorrhage and salmon patches in the right eye.In left eye there was tortuosity of vessels and multiple blot hemorrhage.After 15 days of observation,the hemorrhage was substantially resolved and visual acuity got improved.

Sickle cell retinopathy can occur in patients with sickle cell trait. Treatment modality includes observation and frequent follow up.